ANCA-negative limited Wegener's granulomatosis.
نویسندگان
چکیده
A 26-year-old man presented with epistaxis, nasal obstruction and a subcutaneous swelling over the left malar region with radiological evidence of a mass in the right nasal cavity. Histology of the lesions showed necrotizing granuloma with evidence of vasculitis. There was no other systemic involvement and the patient was ANCA-negative. Excellent response to systemic steroid and cyclophosphamide therapy was noted.
منابع مشابه
Successful Treatment of ANCA-Negative Wegener's Granulomatosis with Rituximab
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عنوان ژورنال:
- Indian journal of dermatology, venereology and leprology
دوره 70 2 شماره
صفحات -
تاریخ انتشار 2004